CCPortal

浏览/检索结果: 共2条,第1-2条 帮助

限定条件    
已选(0)清除 条数/页:   排序方式:
Elesclomol alleviates Menkes pathology and mortality by escorting Cu to cuproenzymes in mice 期刊论文
, 2020, 卷号: 368, 期号: 6491
作者:  Guthrie L.M.;  Soma S.;  Yuan S.;  Silva A.;  Zulkifli M.;  Snavely T.C.;  Greene H.F.;  Nunez E.;  Lynch B.;  de Ville C.;  Shanbhag V.;  Lopez F.R.;  Acharya A.;  Petris M.J.;  Kim B.-E.;  Gohil V.M.;  Sacchettini J.C.
收藏  |  浏览/下载:28/0  |  提交时间:2020/07/28
copper  copper zinc superoxide dismutase  cytochrome c oxidase  dopamine beta monooxygenase  elesclomol  monophenol monooxygenase  protein lysine 6 oxidase  copper  cytochrome c oxidase  elesclomol  hydrazine derivative  copper  cytochrome  enzyme  enzyme activity  mitochondrion  mortality  mutation  pathology  rodent  survival  animal cell  animal experiment  animal model  animal tissue  Article  cohort analysis  controlled study  disease severity  drug mechanism  Golgi complex  H9c2(2-1) cell line  in vivo study  male  Menkes syndrome  mitochondrial dynamics  mortality rate  mouse  nerve degeneration  nonhuman  priority journal  secretory pathway  survival rate  animal  brain  cell line  degenerative disease  disease model  drug effect  genetics  knockout mouse  Menkes syndrome  metabolism  mitochondrion  pathology  rat  transport at the cellular level  Murinae  Mus  Animals  Biological Transport  Brain  Cell Line  Copper  Copper Transporter 1  Disease Models, Animal  Electron Transport Complex IV  Hydrazines  Male  Menkes Kinky Hair Syndrome  Mice  Mice, Knockout  Mitochondria  Neurodegenerative Diseases  Rats  
Endoplasmic reticulum-associated degradation regulates mitochondrial dynamics in brown adipocytes 期刊论文
, 2020, 卷号: 368, 期号: 6486
作者:  Zhou Z.;  Torres M.;  Sha H.;  Halbrook C.J.;  van den Bergh F.;  Reinert R.B.;  Yamada T.;  Wang S.;  Luo Y.;  Hunter A.H.;  Wang C.;  Sanderson T.H.;  Liu M.;  Taylor A.;  Sesaki H.;  Lyssiotis C.A.;  Wu J.;  Kersten S.;  Beard D.A.;  Qi L.
收藏  |  浏览/下载:34/0  |  提交时间:2020/07/28
Hrd1 protein  membrane protein  Sel1L protein  sigma opiate receptor  sigma receptor 1  ubiquitin protein ligase E3  unclassified drug  biodegradation  cell organelle  membrane  mitochondrion  physiology  protein  turnover  animal cell  Article  brown adipocyte  cell contact  controlled study  endoplasmic reticulum  endoplasmic reticulum associated degradation  megamitochondria  mitochondrial dynamics  mitochondrion  mouse  nonhuman  priority journal  protein metabolism  protein protein interaction  thermogenesis  three-dimensional imaging  Mus